Introduction: The association of Hirschsprung’s disease (HD) and anorectal malformation (ARM) is rare. The aim of this study is to highlight the frequency and co morbidity that may be related to this association.
Patients and methods: over a period of ten years eight cases with ARM found to have HD association. All cases were diagnosed by complete clinical, radiological assessment and histopathological examination before correction.
Results: Their age at presentation ranged from 3 days to 10 years. The diagnosis started early during neonatal period only in three cases while in the remaining five cases was delayed either because of atypical symptoms or unsuspected association. Fecal fistula after closure of stoma and wound dehiscence is evident associated co morbidity.
Conclusions: routine rectal biopsy is important after ARM correction and before stoma closure.